Introduction
Waldenström’s macroglobulinemia (VM) is a low-grade B cell lymphoproliferative disorder characterized by a monoclonal synthesis and secretion of immunoglobulin M (Ig M) [1, 2]. Neurologic symptoms are commonly a part of hyperviscosity syndrome or autoimmunologic processes [1, 4]. Rarely, they may result from a direct infiltration of the central nervous system (CNS) by lymphoplasmatoid cells and thus defines the Bing-Neel syndrome (BNS) [1, 2, 3, 4]. This CNS metastasis is commonly a diffuse spreading and a focal tumor like presentation is very rare with usually small size lesions [2, 3 4]. An appearance of a genuine extra axial tumor is very rare in the literature and to the best of our knowledge only 3 cases has been found. We report an incidental discovery of a huge fronto-parietal lesion mimicking a meningioma and referable to a Bing-Neel syndrome after pathological and biological investigations.